PRIMARY CUTANEOUS PERIVASCULAR EPITHELIOID CELL TUMOR (PEComa). CASE REPORT AND REVIEW OF THE LITERATURE

  • Loredana Elena STOICA University of Medicine and Pharmacy of Craiova, Department of Dermatology
  • Rucsandra Cristina DASCĂLU Târgu Cărbunești Hospital, Department of Dermatology
  • Alina Maria VÎLCEA Dunărea de Jos” University of Galati, Romania
  • Gabriela STOLERIU “Dunărea de Jos” University of Galati, Romania
  • Daciana Elena BRĂNIȘTEANU “Grigore T. Popa” University of Medicine and Pharmacy Iasi

Abstract

PEComas represent a family of uncommon mesenchymal tumors that can develop on the skin and also can affect internal organs with a distinct immunophenotype that typically shows both myogenic and melanocytic differentiation. We present the case of a 49 years old female patient, from urban area, who was hospitalized in Dermatology Clinic Craiova for the presence of a 2 cm diameter tumor, round shaped, reddish-pink, with smooth surface, located on the internal site of the right thigh. The diagnosis of primary cutaneous PEComa was confirmed histopathologicaly and immunohistochemically and from the clinical point of view it represents a challenge for the dermatologist.

Author Biographies

Alina Maria VÎLCEA, Dunărea de Jos” University of Galati, Romania

Faculty of Medicine and Pharmacy, Clinical Department

Gabriela STOLERIU, “Dunărea de Jos” University of Galati, Romania

Faculty of Medicine and Pharmacy, Clinical Department

Daciana Elena BRĂNIȘTEANU, “Grigore T. Popa” University of Medicine and Pharmacy Iasi

Faculty of Medicine
Department of Medical Specialties (III)

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Published
2020-09-30
Section
INTERNAL MEDICINE - PEDIATRICS